Hyperimunoglobuline e syndrome: case report
نویسندگان
چکیده
Background Hyperimmunoglobulin E syndrome (HIES) is a rare desease caused by a primary complex immunodeficiency, with IgE serum levels over 2,000U/mL. The syndrome is characterized by the following triad: 1) recurrent staphylococcal abscesses, 2) recurrent airway infections; 3) elevated serum IgE concentration. Our pacient presented signs that are compatible with HIES in distinct moments of his life – microabscesses associated with eczema at adolescence, respiratory infections from childhood until present moment and seric IgE level of over 2,000 in recent dosage.
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عنوان ژورنال:
دوره 8 شماره
صفحات -
تاریخ انتشار 2015